Cart
sales@molnova.com
Glutarylcarnitine
CAS No. 102636-82-8
Glutarylcarnitine( —— )
Catalog No. M33601 CAS No. 102636-82-8
Glutarylcarnitine (O-glutaroyl-L-carnitine) is a diagnostic metabolite for malonic aciduria and glutaric aciduria type I monitored in most tandem mass spectrometry newborn screening programmes.
Purity : >98% (HPLC)
COA
Datasheet
HNMR
HPLC
MSDS
Handing Instructions
| Size | Price / USD | Stock | Quantity |
| 2MG | 74 | Get Quote |
|
| 500MG | Get Quote | Get Quote |
|
| 1G | Get Quote | Get Quote |
|
Biological Information
-
Product NameGlutarylcarnitine
-
NoteResearch use only, not for human use.
-
Brief DescriptionGlutarylcarnitine (O-glutaroyl-L-carnitine) is a diagnostic metabolite for malonic aciduria and glutaric aciduria type I monitored in most tandem mass spectrometry newborn screening programmes.
-
DescriptionGlutarylcarnitine is the diagnostic metabolite for malonic aciduria and glutaric aciduria type I monitored in most tandem mass spectrometry newborn screening programmes.
-
In VitroMalonylcarnitine and Glutarylcarnitine are important diagnostic metabolites in the screening of dried blood spots by tandem mass spectrometry.The urinary excretion of glutarylcarnitine is a specific biochemical marker of glutaric acidemia type I (GA-1). The urinary excretion of glutarylcarnitine is an informative tool in the biochemical diagnosis of glutaric acidemia type I.
-
In Vivo——
-
Synonyms——
-
PathwayProteasome/Ubiquitin
-
TargetEndogenous Metabolite
-
RecptorEndogenous Metabolite
-
Research Area——
-
Indication——
Chemical Information
-
CAS Number102636-82-8
-
Formula Weight275.3
-
Molecular FormulaC12H21NO6
-
Purity>98% (HPLC)
-
SolubilityIn Vitro:?Ethanol : 100 mg/mL (363.24 mM; Ultrasonic)DMSO : 2 mg/mL (7.26 mM; Ultrasonic (<60°C)
-
SMILES[C@H](OC(CCCC(O)=O)=O)(C[N+](C)(C)C)CC([O-])=O
-
Chemical Name——
Shipping & Storage Information
-
Storage(-20℃)
-
ShippingWith Ice Pack
-
Stability≥ 2 years
Reference
1. Johnson DW, et al. Stability of malonylcarnitine and Glutarylcarnitine in stored blood spots. J Inherit Metab Dis. 2004;27(6):789-90.?
molnova catalog
related products
-
Coenzyme Q9
Coenzyme Q9 (CoQ9) is a normal constituent of human plasma.?CoQ9 in human plasma may originate as a product of incomplete CoQ10 biosynthesis or from the diet.
-
Creatine
Creatine is an amino acid that occurs in vertebrate tissues and in urine. In muscle tissue creatine generally occurs as phosphocreatine.
-
5'-Guanylic acid
5'-Guanylic acid is involved in several metabolic disorders, including AICA-ribosiduria pathway, ?adenosine deaminase deficiency,adenine phosphoribosyltransferase deficiency (aprt), and the 2-hydroxyglutric aciduria pathway.
